Rhabdomyosarcoma Arising within Congenital Cystic Adenomatoid Malformation; a Case Report

Amirikar, Farinaz; Bilan, Nemat; Rezamand, Azim; Jamshidi, Masoud; Golchinfar, Zahra

doi:10.22038/ijp.2022.64392.4889

Rhabdomyosarcoma Arising within Congenital Cystic Adenomatoid Malformation; a Case Report

Document Type : case report

Authors

Farinaz Amirikar ¹

Nemat Bilan ¹

Azim Rezamand ²

Masoud Jamshidi ¹

Zahra Golchinfar ³

¹ Pediatric Health Research Center, Tabriz University of Medical Sciences, Tabriz, Iran

² Pediatric Health Research Center, Tabriz University of Medical Sciences, Tabriz, IR Iran

³ Clinical Research Development Unit of Children Educational and Treatment Center, Tabriz University of Medical Sciences, Tabriz, Iran

10.22038/ijp.2022.64392.4889

Abstract

This case report describes a 30-month-old child with primary pulmonary rhabdomyosarcoma with a congenital cystic adenomatoid malformation (CCAM). In the current literature, primary pulmonary neoplasms have been reported for similar cases. The tumor was located in the anterior-basal segment of the left lower lobe with a thin-walled cystic appearance and lobulated margins. A histology examination showed rhabdomyosarcoma origin with an embryonal subtype. Postoperative systemic chemotherapy was carried out. After a 6-month follow-up, the patient had no residual or recurrent disease.

Keywords

Rhabdomyosarcoma

Cystic Adenomatoid

Childhood

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