Sinus Histiocytosis in a Child: A Rare Case Report

Document Type : case report

Authors

1 Department of Paediatrics, Jawaharlal Nehru Medical College, Sawangi Meghe, Wardha, Maharashtra, India.

2 Professor and Head of Department, Dept. of Pediatrics, Jnmc, Sawangi Meghe, Wardha, India.

3 MD, Associate Professor, Department of Pediatrics, Jawaharlal Nehru Medical College, Sawangi, Wardha, India.

Abstract

Background: Rosai-Dorfman disease is a self-limiting condition caused by histiocyte proliferation within the sinusoids of lymph nodes and in the extranodal tissue. It is a rare disease, particularly in children, that progresses with extensive lymphadenopathy.
Case Presentation: We report the case of a 5-year-old child who presented with an enlarged cervical lymph node. Fine Needle Aspiration Cytology (FNAC) was done, which was suggestive of ‘active lymphoid hyperplasia with sinus histiocytosis’
Conclusion: In this case, after careful analysis of the biopsied specimen, a conservative approach was adopted. The patient was discharged and advised for follow-up. On follow-up, after 2 weeks the size of the lymph node had decreased.

Keywords

References

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Journal of Pediatric Perspectives
Volume 12, Issue 8
August 2024
Pages 18984-18987

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