Vulvar lipoblastoma in the utero of a female fetus: A case report

Khanjani, Somayeh; Borna, Sedigheh; Akbari, Razieh; Mirzaeian, Sara; Eshraghi, Nooshin; Nasiri, Seyed Javad; Hashemnejad, Maryam; Pourmahmoodian, Abdolvahab

doi:10.22038/ijp.2021.53471.4242

Vulvar lipoblastoma in the utero of a female fetus: A case report

Document Type : case report

Authors

somayeh khanjani ¹

Sedigheh Borna ²

Razieh Akbari ²

Sara Mirzaeian ³

Nooshin Eshraghi ⁴

Seyed Javad Nasiri ⁵

Maryam Hashemnejad ⁶

Abdolvahab Pourmahmoodian ⁵

¹ Department of Obstetrics and Gynecology, Faculty of Medicine, Isfahan University of Medical Sciences, Isfahan, Iran.

² Department of Obstetrics and Gynecology, Maternal, Faculty of Medicine, Tehran University of Medical Sciences, Tehran, Iran.

³ Department of Obstetrics and Gynecology, Faculty of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran.

⁴ Department of Perinatology, Shahid Akbarabadi Hospital, Faculty of Medicine, Iran University of Medical Sciences, Tehran, Iran.

⁵ Department of Pediatric Surgery, Ali-Asghar Children Hospital, Iran University of Medical Sciences, Tehran, Iran.

⁶ Assistant Professor, Department of Obstetrics and Gynecology, Faculty of Medicine, Alborz University of Medical Sciences, Tehran, Iran.

10.22038/ijp.2021.53471.4242

Abstract

Background: Lipoblastoma is one of the rare masses in childhood and its diagnosis is very uncommon in the perinatal period, so we reported a case with a diagnosis of this mass during pregnancy.
Case Report: In a routine third-trimester ultrasound at 28 weeks, a hyperechoic mass in the size of 27*30mm was detected in between labia majora. However, no abnormal findings were found in perinatal care before this gestational age. Finally, after the birth, at 40 weeks of gestation, the mass was resected and now the baby is in good condition and no recurrence has occurred. There was also an anorectal anomaly associated with this mass in our patient who underwent Anorectoplasty surgery.
Conclusion: Due to the rarity of these tumors, it is important to diagnose them in the perinatal period and to investigate other associated anomalies.

Keywords

Lipoblastoma

perinatal ultrasound

diagnosis

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